Ewing sarcoma is the second most common bone cancer in children and younger adults. However, it is still very rare.
Ewing tumors account for about
This article discusses how common Ewing sarcoma is, statistics, survival rates, and more.
Ewing sarcoma is a
It can develop throughout various locations in the body. Ewing tumors may occur in any bone or soft tissue, but the
Additional statistics for Ewing sarcoma are as follows:
- An estimated 87% of Ewing sarcomas affect the bone. These sarcomas may also affect surrounding soft tissue.
- Ewing sarcoma accounts for
10–15%of all bone sarcomas and less than 5% of all soft tissue sarcomas.
- One-third of all Ewing tumors are present in the pelvis and spine.
The ACS uses a 5-year relative survival rate for people with Ewing sarcoma. This measures the likelihood that a person with Ewing sarcoma will live for at least 5 years after diagnosis, compared with the overall population.
|SEER stage||Stage description||5-year relative survival rate|
|Localized||There are no signs indicating the cancer has spread.||82%|
|Regional||The cancer has spread to nearby structures or lymph nodes.||70%|
|Distant||The cancer reached the lungs or other distant structures.||39%|
|All stages combined||The average of all of the above stages combined.||62%|
For example, people with a localized Ewing tumor are 82% as likely as those without cancer to live for at least 5 years after diagnosis, on average.
Ewing sarcoma cancer can spread — a process known as metastasis — and return, also called recurrence.
The survival rate decreases when the cancer metastasizes, becoming
Along with the stage of cancer, factors that
- size of tumor
- a person’s age
- lactate dehydrogenase (LDH) level
- chemotherapy response
The survival rate of Ewing sarcoma has improved over the past 40 years due to advancements in treatment options, including local and systemic therapies such as chemotherapy and radiation therapy.
However, survival rates are estimates, and the data does not predict what will happen in every case. A person can talk with medical professionals to better understand how individual factors may affect the survival rate.
Ewing sarcoma mainly affects children, teenagers, adolescents, and young adults. Around 80% of people are under 20 years of age at diagnosis.
According to the
Around 30% of Ewing tumors arise in children under 10 years, with another 30% of cases affecting adults over the age of 20. Statistics on Ewing sarcoma in older people remain unknown.
Slightly more males than females develop Ewing sarcoma. Males are about three times more likely to develop Ewing tumors than females.
White adolescents face the highest risk of developing Ewing sarcoma. White people are
Early detection plays a crucial part in the outlook for Ewing sarcoma. According to the American Cancer Society, survival is possible for
If the tumor is present in an extremity, such as an arm or leg, professionals may consider amputation to completely remove all traces of the cancer.
Completely removing a limb means the cancer is less likely to reoccur. Surgically removing Ewing sarcoma on the extremities may be less challenging than treating tumors affecting the chest wall or pelvis.
Therefore, people with Ewing sarcoma in the arm or leg may have a better outlook than those with an Ewing tumor affecting the trunk.
Additionally, those under 10 years of age, a smaller tumor, and typical LDH levels, may have a better outlook.
This section answers common questions about Ewing sarcoma.
What is the leading cause of Ewing sarcoma?
Experts are generally unsure of the cause of Ewing sarcoma. Experts have not found an association between Ewing sarcoma and a family history of cancer, environmental risks, or past exposure to drugs and radiation.
How many cases of Ewing’s sarcoma are there a year?
Between 1973 and 2004, the incidence of Ewing sarcoma in the U.S. was
Ewing sarcoma is a rare form of bone cancer affecting children and young adults. It accounts for about
The survival rate has improved over the last 40 years as a result of advancements in treatment options, such as chemotherapy and radiation therapy.